Acute pulmonary edema due to rupture of mitral valve's posteromedial papillary muscle in a young girl

Abstract

We report a 13-year-old girl with acute pulmonary edema due to severe acute Mitral regurgitation because of rupture of Mitral valve's posteromedial papillary muscle. She had normal mitral valve with necrotic posteromedial papillary muscle, classic aneurysms in left coronary artery, neutrophilic infiltration in the wall of medium-sized vessel of kidney and positive perinuclear antineutrophil cytoplasmic antibodies (P-ANCA) a diagnosis of polyarteritis nodosa. She treated successfully with mitral valve replacement.