Anesthesia management of a patient with papillon-lefevre syndrome: A case report

Abstract

Introduction: Papillon-Lefأ¨vre syndrome (PLS) is a rare autosomal recessive trait; it often requires some interventions with general anesthesia because of the accompanied complications. Case Presentation: We report a 19-year-old girl with palmoplantar hyperkeratosis who presented total loss of her teeth. She was candidate to mandibular bone graft and lower jaw dental implants under general anesthesia. Conclusions: There are only a few studies about perioperative management of these patients; however, the anesthesiologists should consider a few important issues during pre-operative and intra-operative management. آ© 2016, Iranian Society of Regional Anesthesia and Pain Medicine (ISRAPM).