Prevalence of Long QT Syndrome in Children with Congenital Deafness (Sensory - Neural)

Abstract

Long QT syndrome (LQTS) is characterized by prolonged QT time associated with syncope attacks and sudden death. Jervell and Lange-Nielsen first described LQTS in conjunction with sensory-neural birth defect. Since the number of people with congenital deafness in the society is not low and studies in Iran about this syndrome especially in children are limited and considering the identification of these patients by performing ECG and simple measures, it can be concluded that their sudden death can be significantly reduced. Preventing attention, the aim of this study was to determine the prevalence of prolonged QT syndrome in children with congenital sensory-neural deafness in patients undergoing cochlear implant surgery. Materials and Methods: In this cross-sectional retrospective observational study, all children with congenital deer undergoing cochlear implantation were enrolled. Patients' heart rate and prolonged QT after calculating QT were evaluated using Bazett's formula and its association with suppression and sudden death, and finally diagnosed using Schwartz's Kriti of children with long QT syndrome. Its association with the congenital Kerry was evaluated. Results: Of the 357 patients studied, 204 (57.1%) were male and 153 (42.9%) were female. The mean ± SD of the current age of the patients was 7.15±2.93 years with a mean of 7 years. The mean ± SD of QT interval in the studied patients was 291.01±26.89 ms with a mean of 280 ms. The mean ± SD of QTc interval in the studied patients was 400.52±25.74 ms with a median of 404 ms. Frequency of Long QTc in the studied patients was 17 cases (4.8%).